ISSN: 2161-0533
Demet Dogan Erol, Alper Kaya and Burak Akan
Osteogenesis imperfecta which is also known as Vrolik’s disease is a connective tissue disorder associated with many potential problems; fragile bones and teeth, abnormal airway, megalocephaly, macroglossia, short neck, thoracic deformities, susceptibility to malignant hyperthermia, hyperthyroidism, congenital cardiac diseases, emphysema and bleeding disorders due to platelet dysfunction are the most prominent problems concerning anesthesia management. This patients should presented for an elective surgical procedure, a careful history should revealed the details of illness that guided us to do the minimal essential investigations that would suffice to exclude any existing problems and thereby provide safe anaesthesia.
We report the anesthetic and operative management of a patient in which osteotomy and intramedullary nailing were performed under general anesthesia with regard to recently new anesthetic agents and techniques.