Cardiologia Clínica e Experimental
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Cor Triatriatum Sinister and Patent Ductus Arteriosus in a 23 year-old Filipino

Aila V. Velasco

Cor triatriatum is a rare cardiac condition involving the left atrium, representing only 0.1-0.4% of all congenital heart diseases. It presents as one of the atrium being divided into two chambers by a fibromuscular membrane and classically appear on the left atrium.
We report the case of a 23-year old Filipino female with orofacial cleft, presenting with symptoms of decompensated heart failure. Clinical examination revealed the presence of diastolic murmur, 5/6, with accentuated pulmonary component of the second heart sound. Cardiomegaly was seen on chest x-ray and right ventricular hypertrophy on electrocardiogram. Transthoracic echocardiogram (TTE) shows Cor triatrium sinistrum; dilated left atrium divided by a membrane into a proximal and distal chamber; dilated right atrium; dilated right ventricle with right ventricular hypertrophy; dilated main pulmonary artery; and severe pulmonic regurgitation with severe pulmonary hypertension.