ISSN: 2155-9554
Pancham Kumar and Rohit Vohra
Kasabach-Merritt Syndrome (KMS) is a rare disorder that can affect infants from the time of birth or later in infancy. Diagnosis of KMS is made based on the constellation of hemangioma, thrombocytopenia, and coagulopathy. Our case presented at birth with hemangioma on perineal area and bleeding tendancy. On evaluation thrombocytopenia and coaguloepathy were found and diagnosis KMS was established supported by histopathology. Baby was treated with oral predinisolone and showed complete resolution of hemangioma and normalization of lab parameters.