Anestesia e Pesquisa Clínica
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Abstrato

Anesthetic Considerations in Pediatric Patients with Epidermolysis Bullosa: A Case Report

Sung-Mi Ji, Sung-Man Hong, Chae-Min Cho, Min-A Kwon and Seok-kon Kim

Epidermolysis bullosa (EB), a rare genetic disorder with abnormal fragility of skin and mucous membranes, is characterized by blister formation, either spontaneously or following a minor friction. In addition to the skin, it often involves other epithelial-lined organs requiring profound considerations in the anesthetic management related to some comorbidities. Monitoring, difficult airway, positioning, nutritional deficiencies and poor immunity can be challenging for the anesthesiologist in perioperative management. The authers described an experience of a 3-year-old male child with a dystrophic type of EB since birth who underwent hernioplasty. Perioperative careful management and minimal mandatory monitoring might be needed to minimize mechanical injury to the skin and mucous membranes.