Anestesia e Pesquisa Clínica
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Anesthetic Management of Congenital Insensitivity to Pain with Anhidrosis in a Child: A Case Report

Yanruo Huang, Anmin Hu, Ye Jiang, Yunxia Zuo and Guizhi Du

Background: Congenital insensitivity to pain with anhidrosis (CIPA) is a rare hereditary sensory autonomic neuropathy. Anesthetic management of those patients is challenging for anesthesiologist because of the potential risks for them including regurgitation and aspiration, sympathetic nervous dysfunction, mandibular osteomyelitis as well as hyperthermic events.

Case report: We present total intravenous anesthesia (TIVA) with spontaneous respiration via facemask was applied in a 2 y old child with CIPA who underwent closed reduction and plaster external fixation of a bilateral dislocation of the hip. The patient vital signs remained stable, and did not show any signs of distress by anesthetics during the surgery. And no complication occurred.

Conclusion: TIVA with spontaneous respiration via facemask is an effective and safe anesthetic management for patients with CIPA.